亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質(zhì)量反饋  關于我們  聯(lián)系我們
无码av中文字幕免费放,91嫖妓站街按摩店老熟女
首頁 > 產(chǎn)品中心 > 一抗 > 產(chǎn)品信息
PLP1 Mouse mAb (bsm-51197M)  
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
50ul/1580.00元
100ul/2500.00元
大包裝/詢價
產(chǎn)品編號 bsm-51197M
英文名稱 PLP1 Mouse mAb
中文名稱 髓磷酯髓鞘蛋白1單克隆抗體
別    名 MYPR_HUMAN; Myelin proteolipid protein; PLP; Lipophilin; proteolipid protein 1; PMD; HLD1; MMPL; SPG2; GPM6C; PLP/DM20;  
研究領域 神經(jīng)生物學  細胞粘附分子  
抗體來源 Mouse
克隆類型 Monoclonal
克 隆 號 40000000
交叉反應 (predicted: Human,Rat)
產(chǎn)品應用 WB=1:500-2000
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
理論分子量 30 kDa
檢測分子量
細胞定位 細胞膜 
性    狀 Liquid
濃    度 1mg/1ml
免 疫 原 KLH conjugated synthetic peptide derived from rat PLP1: 201-277/277 
亞    型 IgM
純化方法 affinity purified by Protein AGL
緩 沖 液 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
保存條件 Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.
注意事項 This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
PubMed PubMed
產(chǎn)品介紹 PLP is a major constituent of myelin. The two isoforms of the myelin proteolipid protein, PLP and DM20, are very hydrophobic integral membrane proteins that account for about half of the protein content of adult CNS myelin. A mutation in the gene which encodes PLP is linked to Pelizaeus-Merzbacher disease (PMD), a chronic infantile type of diffuse cerebral sclerosis. The gene which encodes PLP maps to human chromosome Xq22. The glycoprotein zero (also designated P-zero or myelin peripheral protein) is the primary structural protein of peripheral myelin, and accounts for more than 50% of the protein present in the peripheral nerve sheath. Zero is an integral membrane glycoprotein. Expression of zero is restricted to Schwann cells. The gene which encodes zero maps to human chromosome 1q22. PMP22 (peripheral myelin protein 22) is a growth-regulated membrane protein which is expressed by Schwann cells and is localized primarily in compact peripheral nervous system myelin. The gene which encodes PMP22 maps to human chromosome 17p11.2.

Function:
This is the major myelin protein from the central nervous system. It plays an important role in the formation or maintenance of the multilamellar structure of myelin.

Subunit:
Belongs to the myelin proteolipid protein family.

Subcellular Location:
Membrane; Multi-pass membrane protein.

DISEASE:
Defects in PLP1 are the cause of leukodystrophy hypomyelinating type 1 (HLD1) [MIM:312080]; also known as Pelizaeus-Merzbacher disease. HLD1 is an X-linked recessive dysmyelinating disorder of the central nervous system in which myelin is not formed properly. It is characterized clinically by nystagmus, spastic quadriplegia, ataxia, and developmental delay.
Defects in PLP1 are the cause of spastic paraplegia X-linked type 2 (SPG2) [MIM:312920]. SPG2 is characterized by spastic gait and hyperreflexia. In some patients, complicating features include nystagmus, dysarthria, sensory disturbance, mental retardation, optic atrophy.

Similarity:
Belongs to the myelin proteolipid protein family.

SWISS:
P60203

Gene ID:
24943

Database links:

Entrez Gene: 281410 Cow

Entrez Gene: 481002 Dog

Entrez Gene: 5354 Human

Entrez Gene: 18823 Mouse

Entrez Gene: 24943 Rat

Omim: 300401 Human

SwissProt: P04116 Cow

SwissProt: P23294 Dog

SwissProt: P60201 Human

SwissProt: P60202 Mouse

SwissProt: P60203 Rat

Unigene: 49691 Cow

Unigene: 1787 Human

Unigene: 1268 Mouse

Unigene: 4550 Rat



版權所有 2004-2026 www.a6308.cn 北京博奧森生物技術有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
亚洲AV午夜福利无码精品一区 | 兰桂坊人成社区亚洲精品 | 日本韩国做暖暖小视频 | 高清一级毛片一本到免费观看 | 成 人3d动漫在线观看 | 国产精品免费大片 | 高跟丝袜人妖ts被虐调教 | 直接看的av网址免费的 | 亚洲高清无码在线观看 | 国产情侣2020免费视频 | 性欧美熟妇freetube | XX性欧美肥妇精品久久久久久 | 老头埋进校花里面使劲添 | 女性高爱潮有声视频A片 | 欧美性大战xxxxx久久久 | 一区二区三区囯产精品乱码不卡 | 99热门精品一区二区 | 教室啪啪高挑长腿正在播放 | 国产精品亚洲第一区在线 | 欧美自拍另类欧美综合图片区 | 国产美女69视频免费观看 | 国产乱妇乱子在线播放视频 | 一牛影视传媒有限公司官网 | 国产成人无码精品久久久APP | 精产国蘑菇品一二三产品区 | 大屁股国产白浆一二区 | 久久综合色一综合色88 | 日韩精品极品视频在线观看免费 | 国模大胆一区二区三区 | 欧美成人精品欧美一级乱黄 | 黄色网站在线观看免费 | www免费视频在线观看播放 | 中国女人一级毛片 | 国产品无码一区二区三区在线 | 精品国产aⅴ无码一区二区91 | 亚洲AV无码一区二区二三区 | 99久在线国内在线播放免费观看 | 真实人与人性恔配视频 | 国产特级淫片免费看欧美日韩中文 | 色哟哟国产精品一区二区真心好看 | 亚洲人成aⅴ在线播放 |