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Rabbit Anti-beta Sarcoglycan/BF594 Conjugated antibody (bs-1127R-BF594)
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說(shuō) 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-1127R-BF594
英文名稱 Rabbit Anti-beta Sarcoglycan/BF594 Conjugated antibody
中文名稱 BF594標(biāo)記的肌聚多糖-β抗體
別    名 beta Sarcoglycan; beta-sarcoglycan; Sarcoglycan beta; BETA SARCOGLYCAN; A3b; LGMD2E; SGC; 43 kDa dystrophin associated glycoprotein; 43DAG; A3b; Beta SG; LGMD2E; SGC; SGCB; AI747103; AI844814; LOC687025; SGCB_HUMAN; Beta-sarcoglycan; Beta-SG; 43 kDa dystrophin-associated glycoprotein.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說(shuō) 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  免疫學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  糖蛋白  
抗體來(lái)源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng)
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 35kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human SGCB
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a member of the sarcoglycan family. Sarcoglycans are transmembrane components in the dystrophin-glycoprotein complex which help stabilize the muscle fiber membranes and link the muscle cytoskeleton to the extracellular matrix. Mutations in this gene have been associated with limb-girdle muscular dystrophy.

Function:
Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix. Tissue specificity: Highest expression in heart and skeletal muscle. Low expression in brain, kidney, placenta, pancreas and lung. High expression in fetal brain. Also found in fetal lung, kidney and liver. PTM: Disulfide bonds are present By similarity. Sequence similarities: Belongs to the sarcoglycan beta/delta/gamma/zeta family.

Subcellular Location:
Cell membrane; sarcolemma; single-pass type II membrane protein. Cytoplasm; cytoskeleton

Database links:

Entrez Gene: 6443 Human

Omim: 600900 Human

SwissProt: Q16585 Human

Unigene: 438953 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
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