亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
国偷自产AV一区二区三区健身房,国精产品自线在拍在线看,国产三级级在线观看大学生
Rabbit Anti-ATXN3L/HRP Conjugated antibody (bs-4807R-HRP)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-4807R-HRP
英文名稱 Rabbit Anti-ATXN3L/HRP Conjugated antibody
中文名稱 辣根過氧化物酶標(biāo)記的小腦脊髓共濟(jì)失調(diào)蛋白3抗體
別    名 ATX3L_HUMAN; ATXN3L; Machado-Joseph disease protein 1-like; MJDL; Putative ataxin-3-like protein.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  免疫學(xué)  染色質(zhì)和核信號  表觀遺傳學(xué)  泛素  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, )
產(chǎn)品應(yīng)用 WB=1:500-2000 IHC-P=1:50-200 IHC-F=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 41kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ATXN3L
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Defects in ATXN3 are the cause of spinocerebellar ataxia type 3 (SCA3) ; also known as Machado-Joseph disease (MJD). Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders. Patients show progressive incoordination of gait and often poor coordination of hands, speech and eye movements, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord. SCA3 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, ophthalmoplegia, bulbar and extrapyramidal signs, peripheral neuropathy and dementia. The molecular defect in SCA3 is the a CAG repeat expansion in ATXN3 coding region. Longer expansions result in earlier onset and more severe clinical manifestations of the disease.

Function:
Deubiquitinating enzyme that cleaves both 'Lys-48'-linked and 'Lys-63'-linked poly-ubiquitin chains (in vitro).

Subcellular Location:
Nucleus (By similarity).

Similarity:
Contains 1 Josephin domain.
Contains 2 UIM (ubiquitin-interacting motif) repeats.

Database links:
UniProtKB/Swiss-Prot: Q9H3M9.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
豆奶视频在线观看免费高清版 | 1区2区3区产品乱码免费 | 精品乱码一区内射人妻无码 | 国产剧情福利AV一区二区 | 国产欧美一区二区精品仙草咪 | 欧美成人久久一级c片免费 免费视频国产在线观看 | 自拍偷在线精品自拍无码专区 | 老妇又粗又大舒服极了 | 日韩三级中文字幕 | 日本高清在线天码一区播放 | 亚洲日韩一区精品射精 | 综合精品欧美日韩在线观看 | 玩50岁四川熟女大白屁股直播 | 欧美在线成人免费观看网站 | 无码不卡中文字幕一区二区三区 | 国产综合成人久久大片91 | 日本乱妇乱子视频 | 91欧洲在线视精品在亚洲 | 欧美在线成人免费观看网站 | 国产午夜无码91精品免费看 | 欧美巨鞭大战丰满少妇 | 成 人影片 免费观看 | 亚欧色一区W666天堂 | 一级a性色生活片久久无码火 | 免费无码又爽又黄又刺激网站 | 恩恩呜呜好大好爽快点 | 欧美亚洲精品中文字幕乱码免费高清 | 久久久久久久精品一区二区三区 | 精品久久久亚洲精品中文字幕 | 久久夜色精品国产噜噜亚洲av | 真实国产乱人伦在线视频播放 | 少妇人妻偷人精品视蜜桃 | 日本一道高清一区二区三区 | 国产亚洲欧美日韩综合综合二区 | 羞羞视频在线免费观看 | 十八岁以下禁止观看的1000个网站 | 男女一级毛片免费视频看 | 日本国产一区二区三区 | 免费看高视频hh网站免费 | 欧美精品久久久久久久小说 | 欧美性爱视频在线播放 |