亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
国偷自产AV一区二区三区健身房,国精产品自线在拍在线看,国产三级级在线观看大学生
Rabbit Anti-ATXN3L/HRP Conjugated antibody (bs-4807R-HRP)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-4807R-HRP
英文名稱 Rabbit Anti-ATXN3L/HRP Conjugated antibody
中文名稱 辣根過氧化物酶標(biāo)記的小腦脊髓共濟(jì)失調(diào)蛋白3抗體
別    名 ATX3L_HUMAN; ATXN3L; Machado-Joseph disease protein 1-like; MJDL; Putative ataxin-3-like protein.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  免疫學(xué)  染色質(zhì)和核信號  表觀遺傳學(xué)  泛素  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, )
產(chǎn)品應(yīng)用 WB=1:500-2000 IHC-P=1:50-200 IHC-F=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 41kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ATXN3L
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Defects in ATXN3 are the cause of spinocerebellar ataxia type 3 (SCA3) ; also known as Machado-Joseph disease (MJD). Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders. Patients show progressive incoordination of gait and often poor coordination of hands, speech and eye movements, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord. SCA3 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, ophthalmoplegia, bulbar and extrapyramidal signs, peripheral neuropathy and dementia. The molecular defect in SCA3 is the a CAG repeat expansion in ATXN3 coding region. Longer expansions result in earlier onset and more severe clinical manifestations of the disease.

Function:
Deubiquitinating enzyme that cleaves both 'Lys-48'-linked and 'Lys-63'-linked poly-ubiquitin chains (in vitro).

Subcellular Location:
Nucleus (By similarity).

Similarity:
Contains 1 Josephin domain.
Contains 2 UIM (ubiquitin-interacting motif) repeats.

Database links:
UniProtKB/Swiss-Prot: Q9H3M9.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
亚洲日本久久久午夜精品 | 免费精品国产自产拍在线观看图片 | hot亚洲欧美日韩精品久久视频在线播放 | 亚洲熟女乱色一区二区三区 | 97精品国产高清自在线看超 | 全黄H全肉短篇禁乱NP慕浅浅 | 国产午夜一级鲁丝片 | 亚洲欧美日韩成人在线 | 连续高潮抽搐爽死喷水流白浆无码 | 国产欧美一区二区三区不卡 | 女人高潮久久久叫人喷水 | av高清无码网址大全 | √天堂中文在线最新版 | 亚洲成人电影在线观看精品国产 | 久久久精品中文字幕麻豆发布 | 性妇WBBBB搡BBBB嗓小说 | 欧美综合中文字幕久久99 | 成人MV射精无打码视频 | 水野优香vagu224在线播放 | 国产乱妇乱子视频在线播放国产 | 久久久久人妻精品一区5555 | 国产欧美日韩一区二区搜索 | 国产V片在线播放免费无码 日韩在线视频一区二区三区 | 亚洲一区免费观看 | 久久精品自慰喷水一区二区下载 | 又黄又湿免费高清视频 | 在线综合亚洲欧美网站无弹窗 | 欧美三级在线电影免费 | 国内大量揄拍人妻在线视频 | 久久久久亚洲视频 | 91精品国产高清91久久久久久 | 久久久精品国产亚洲AV无码 | 成人H动漫精品一区二区无码 | 国产成人精品久久一区二区三区 | 玩50岁四川熟女大白屁股直播 | 欧美高清视频www夜色资源网 | 麻婆豆传媒一区二区三区 | 日韩高清成片免费视频 | 精品国产污污免费网站入口在线 | 国产在线a免费观看 | 探花口爆颜射乳交日韩 |