亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
日本在线视频一区,午夜色大片在线观看,在线观看国产精品第一区免费
Rabbit Anti-HADHSC/Cy5.5 Conjugated antibody (bs-10020R-Cy5.5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-10020R-Cy5.5
英文名稱 Rabbit Anti-HADHSC/Cy5.5 Conjugated antibody
中文名稱 Cy5.5標(biāo)記的短鏈L-3羥烷基輔酶A脫氫酶抗體
別    名 HAD; HADH; HADH1; HADHSC; HCDH; HCDH_HUMAN; HHF4; Hydroxyacyl CoA dehydrogenase; Hydroxyacyl-coenzyme A dehydrogenase; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial; L 3 hydroxyacyl Coenzyme A dehydrogenase short chain; M SCHAD; Medium and short chain L 3 hydroxyacyl coenzyme A dehydrogenase; Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; MGC8392; mitochondrial; MSCHAD; OTTHUMP00000162626; OTTHUMP00000219688; SCHAD; Short chain 3 hydroxyacyl CoA dehydrogenase mitochondrial; short chain 3-hydroxyacyl-coa dehydrogenase; Short-chain 3-hydroxyacyl-CoA dehydrogenase.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  信號(hào)轉(zhuǎn)導(dǎo)  激酶和磷酸酶  糖尿病  新陳代謝  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Mouse, Rat,  (predicted: Human, Pig, Cow, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 33kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HADHSC
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene is a member of the 3-hydroxyacyl-CoA dehydrogenase gene family. The encoded protein functions in the mitochondrial matrix to catalyze the oxidation of straight-chain3-hydroxyacyl-CoAs as part of the beta-oxidation pathway. Its enzymatic activity is highest with medium-chain-length fatty acids. Mutations in this gene cause one form of familial hyperinsulinemic hypoglycemia. The human genome contains a related pseudogene of this gene on chromosome 15. [provided by RefSeq.]

Function:
Plays an essential role in the mitochondrial beta-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion matrix.

Tissue Specificity:
Expressed in liver, kidney, pancreas, heart and skeletal muscle.

DISEASE:
Defects in HADH are the cause of 3-alpha-hydroxyacyl-CoA dehydrogenase deficiency (HADH deficiency) [MIM:231530]. HADH deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.
Defects in HADH are the cause of familial hyperinsulinemic hypoglycemia type 4 (HHF4) [MIM:609975]; also known as persistent hyperinsulinemic hypoglycemia of infancy (PHHI) or congenital hyperinsulinism. HHF is the most common cause of persistent hypoglycemia in infancy and is due to defective negative feedback regulation of insulin secretion by low glucose levels. It causes nesidioblastosis, a diffuse abnormality of the pancreas in which there is extensive, often disorganized formation of new islets. Unless early and aggressive intervention is undertaken, brain damage from recurrent episodes of hypoglycemia may occur. HHF4 should be easily recognizable by analysis of acylcarnitine species and that this disorder responds well to treatment with diazoxide. It provides the first 'experiment of nature' that links impaired fatty acid oxidation to hyperinsulinism and that provides support for the concept that a lipid signaling pathway is implicated in the control of insulin secretion.

Similarity:
Belongs to the 3-hydroxyacyl-CoA dehydrogenase family.

Database links:

Entrez Gene: 3033 Human

Entrez Gene: 15107 Mouse

Entrez Gene: 113965 Rat

Omim: 601609 Human

SwissProt: Q16836 Human

SwissProt: Q61425 Mouse

SwissProt: Q9WVK7 Rat

Unigene: 438289 Human

Unigene: 260164 Mouse

Unigene: 92789 Rat




Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
亚洲中文字幕在线一区播放 | 日韩欧美一及在线播放 | 亚洲日韩国产成在线发布一区二区三区 | 成人免费大片黄在线播放 | 国产精品高潮久久久久无码 | 久久国产精品99久久久久久老狼 | 狠狠躁日日躁夜夜躁2022麻豆 | 欧美日韩不卡合集视频 | 亚洲第一天堂WWW网站 | 美妇吞吐粗长撞击迎合 | 一个人免费观看视频www | 粉嫩METART人体欣赏 | 无码精品人妻一区二区三区涩爱 | 亚洲精品无码av中文字幕网站 | 99无码熟妇丰满人妻啪啪 | 国偷自产AV一区二区三区健身房 | 毛片视频在线免费观看 | 99精品一级欧美片免费播放 | 五月丁香久久伊人本道开心 | 高h原耽肉汁动漫视频 | 很狠干线观看2021 | 一本久久综合亚洲鲁鲁五月天 | 欧美又大又粗又硬BBBBB小说 | 国产精品青青青高清在线 | 欧美乱妇日本无乱码特黄大片 | 巜豪妇荡乳2在线观看 | 99精品久久久久久人妻精品 | 国产v综合v亚洲欧美大片 | 色欲av伊人久久大香线蕉影院 | 中文字幕无码家庭乱欲 | 国产99视频在线观看 | 无码人妻精品一区二区中文 | 成AV免费大片黄在线观看 | WWW成人国产高清内射 | 成人免费毛片AAAAAA片 | 欧美精品黄页在线观看大全 | 亚洲AV一宅男色影视 | 日韩欧美一区二区三区久久婷婷 | 99re热线精品视频 | 国产在线观看www | 扒开老师大腿猛进AAA片软件 |