亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
国产精品白浆无码流出.在线观看,久激情内射婷内射蜜桃人妖,国产精品一区二区久久宅男宅女
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-HADHSC/APC Conjugated antibody (bs-10020R-APC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-10020R-APC
英文名稱 Rabbit Anti-HADHSC/APC Conjugated antibody
中文名稱 APC標記的短鏈L-3羥烷基輔酶A脫氫酶抗體
別    名 HAD; HADH; HADH1; HADHSC; HCDH; HCDH_HUMAN; HHF4; Hydroxyacyl CoA dehydrogenase; Hydroxyacyl-coenzyme A dehydrogenase; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial; L 3 hydroxyacyl Coenzyme A dehydrogenase short chain; M SCHAD; Medium and short chain L 3 hydroxyacyl coenzyme A dehydrogenase; Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; MGC8392; mitochondrial; MSCHAD; OTTHUMP00000162626; OTTHUMP00000219688; SCHAD; Short chain 3 hydroxyacyl CoA dehydrogenase mitochondrial; short chain 3-hydroxyacyl-coa dehydrogenase; Short-chain 3-hydroxyacyl-CoA dehydrogenase.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細胞生物  信號轉(zhuǎn)導  激酶和磷酸酶  糖尿病  新陳代謝  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Mouse, Rat,  (predicted: Human, Pig, Cow, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 33kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HADHSC
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene is a member of the 3-hydroxyacyl-CoA dehydrogenase gene family. The encoded protein functions in the mitochondrial matrix to catalyze the oxidation of straight-chain3-hydroxyacyl-CoAs as part of the beta-oxidation pathway. Its enzymatic activity is highest with medium-chain-length fatty acids. Mutations in this gene cause one form of familial hyperinsulinemic hypoglycemia. The human genome contains a related pseudogene of this gene on chromosome 15. [provided by RefSeq.]

Function:
Plays an essential role in the mitochondrial beta-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

Subunit:
Homodimer.

Subcellular Location:
Mitochondrion matrix.

Tissue Specificity:
Expressed in liver, kidney, pancreas, heart and skeletal muscle.

DISEASE:
Defects in HADH are the cause of 3-alpha-hydroxyacyl-CoA dehydrogenase deficiency (HADH deficiency) [MIM:231530]. HADH deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.
Defects in HADH are the cause of familial hyperinsulinemic hypoglycemia type 4 (HHF4) [MIM:609975]; also known as persistent hyperinsulinemic hypoglycemia of infancy (PHHI) or congenital hyperinsulinism. HHF is the most common cause of persistent hypoglycemia in infancy and is due to defective negative feedback regulation of insulin secretion by low glucose levels. It causes nesidioblastosis, a diffuse abnormality of the pancreas in which there is extensive, often disorganized formation of new islets. Unless early and aggressive intervention is undertaken, brain damage from recurrent episodes of hypoglycemia may occur. HHF4 should be easily recognizable by analysis of acylcarnitine species and that this disorder responds well to treatment with diazoxide. It provides the first 'experiment of nature' that links impaired fatty acid oxidation to hyperinsulinism and that provides support for the concept that a lipid signaling pathway is implicated in the control of insulin secretion.

Similarity:
Belongs to the 3-hydroxyacyl-CoA dehydrogenase family.

Database links:

Entrez Gene: 3033 Human

Entrez Gene: 15107 Mouse

Entrez Gene: 113965 Rat

Omim: 601609 Human

SwissProt: Q16836 Human

SwissProt: Q61425 Mouse

SwissProt: Q9WVK7 Rat

Unigene: 438289 Human

Unigene: 260164 Mouse

Unigene: 92789 Rat




Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
久久精品九九亚洲精品 | 国产精品高清视亚洲一区二区 | 亚洲AV一宅男色影视 | 色偷偷噜噜噜亚洲男人 | 欧美最猛激情性AAAAA | 少妇被躁爽到高潮无码文 | 久久成人无码国产免费播放 | 被CAO哭高H野外NP小说男男 | 亚洲欧美日韩国产综合五月天 | 四虎国产精品永久地址入口 | 中国一级免费毛片 | 免费下载黄色app | 国产伦精品一区二区三区免费 | 麻豆果冻精东九一传媒MV | 在线永久免费观看黄网站 | 免费国产黄网在线观看 | 在线视频精品免费观看10 | 91在线视频免费播放 | 内射中出日韩无国产剧情 | 亚洲国产精品成人综合色GIF | 人妻性奴波多野结衣无码 | 日韩视频在线精品视频免费观看 | 国产精品日韩AV无码久久 | 色婷婷色综合缴情网站 | 成人无码片黄网站A毛片免费 | 欧美一级特黄aaaaaa在线看首页 | 国产黄片高清无码在线观看 | 加勒比色综合久久久久久久久 | 欧美freesex黑人又粗又大 | 国内精品一区二区综合欧美 | 一级毛片在线免费视频 | 亚洲v无码专区国产乱码一区二区 | 一个色综合国产色综合 | 亚洲AⅤ永久无码精品毛片费观看 | 亚洲精品永久在线观看 | 亚洲综合色区另类aV无码 | 亚洲AV成人无码网天堂 | 国产AV无码专区毛片 | 日韩一区二区在线观看视频 | 久久久久亚洲精品天堂久久久久久 | 日韩欧无码一区二区三区免费不卡 |