亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號(hào)           掃碼咨詢(xún)技術(shù)支持           掃碼咨詢(xún)技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
97精品一区二区视频在线观看,国产成人亚洲精品无码A大片
Rabbit Anti-MTMR13/PE Conjugated antibody (bs-17249R-PE)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@bioss.com.cn
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說(shuō) 明 書(shū): 100ul  
100ul/2980.00元
大包裝/詢(xún)價(jià)
產(chǎn)品編號(hào) bs-17249R-PE
英文名稱(chēng) Rabbit Anti-MTMR13/PE Conjugated antibody
中文名稱(chēng) PE標(biāo)記的肌微管蛋白MTMR13抗體
別    名 SBF2; CMT4B2; KIAA1766; MTMR13; Myotubularin-related protein 13; SET-binding factor 2.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買(mǎi)        大包裝/詢(xún)價(jià)
說(shuō) 明 書(shū) 100ul  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  G蛋白信號(hào)  
抗體來(lái)源 Rabbit
克隆類(lèi)型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Horse, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 208kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human MTMR13
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a pseudophosphatase and member of the myotubularin-related protein family. This gene maps within the CMT4B2 candidate region of chromosome 11p15 and mutations in this gene have been associated with Charcot-Marie-Tooth Disease, type 4B2. [provided by RefSeq, Jul 2008]

Function:
Defects in SBF2 are the cause of Charcot-Marie-Tooth disease type 4B2 (CMT4B2). CMT4B2 is a recessive form of Charcot-Marie-Tooth disease, the most common inherited disorder of the peripheral nervous system. Charcot-Marie-Tooth disease is classified in two main groups on the basis of electrophysiologic properties and histopathology: primary peripheral demyelinating neuropathy and primary peripheral axonal neuropathy. Demyelinating CMT neuropathies are characterized by severely reduced nerve conduction velocities (less than 38 m/sec), segmental demyelination and remyelination with onion bulb formations on nerve biopsy, slowly progressive distal muscle atrophy and weakness, absent deep tendon reflexes, and hollow feet. By convention, autosomal recessive forms of demyelinating Charcot-Marie-Tooth disease are designated CMT4. CMT4B2 is characterized by abnormal folding of myelin sheaths. CMT4B2 is a recessive form of Charcot-Marie-Tooth disease, the most common inherited disorder of the peripheral nervous system. Charcot-Marie-Tooth disease is classified in two main groups on the basis of electrophysiologic properties and histopathology: primary peripheral demyelinating neuropathy and primary peripheral axonal neuropathy. Demyelinating CMT neuropathies are characterized by severely reduced nerve conduction velocities (less than 38 m/sec), segmental demyelination and remyelination with onion bulb formations on nerve biopsy, slowly progressive distal muscle atrophy and weakness, absent deep tendon reflexes, and hollow feet. By convention, autosomal recessive forms of demyelinating Charcot-Marie-Tooth disease are designated CMT4. CMT4B2 is characterized by abnormal folding of myelin sheaths.

Subcellular Location:
Cell Membrane and Cytoplasmic. Peripheral membrane protein.

Database links:

Entrez Gene: 81846 Human

Omim: 607697 Human

SwissProt: Q86WG5 Human

Unigene: 577252 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書(shū)編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書(shū)編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
WWW夜片内射视频在观看视频 | 在线观看国产精品女主播 | 岳每晚被弄得嗷嗷叫高潮 | 久久婷婷五月综合丁香人人爽 | 日韩经典午夜福利发布 | 亚洲人成人网毛片在线播放 | 香港三级精品三级在线专区 | jk黑色丝袜美腿老师啪啪 | 国产欧美精品123区发布 | 亚洲无吗在线视频 | 视频一本大道香蕉久在线播放 | 99久久这里只精品国产免费 | 高清有码国产一区二区 | 国产精品高潮久久久久久无码 | 国产品无码一区二区三区在线 | 久久综合色天天久久综合图片 | 亚洲AV成人影视在线观看 | 为您提供久久久久精品免费看 | 有码中文无码中文无码人妻 | 国产精品久久久久久无码人疌 | 777久久国产精品无码专区 | 高潮毛片无遮挡免费高清 | 99亚洲男女激情在线观看 | 国产精品久久一区二区三蜜桃 | 18成禁人视频免费午夜影视 | 又黄又湿真实网站不付费 | 调教我的妺妺H肉YIN荡视频 | 亚洲精品视频在线免费观看 | 456亚洲人成影视在线观看 | 国产AVXXXX无套内射 | 日本精品久久久久中文字幕 | 久久人做人爽一区二区三区 | 91精品91免费观看 | 国产欧美日韩专区发布 | 一本大道加勒比久久 | 男人TV天堂精品一区二区 | 熟妇人妻中文字幕无码老熟妇 | 国产成人精品久久久亚洲综合一区色婷婷 | 黑人啊灬啊灬啊灬快灬深 | 欧美日韩免费在线 | 9久9久女女免费视频精品 |