亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質(zhì)量反饋  關于我們  聯(lián)系我們
五月天丁香婷深爱综合,亚洲中文字幕AV在天堂,少妇被躁爽到高潮无码麻豆AV
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-mucolipin 1/FITC Conjugated antibody (bs-18731R-FITC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-18731R-FITC
英文名稱 Rabbit Anti-mucolipin 1/FITC Conjugated antibody
中文名稱 FITC標記的粘脂蛋白1抗體
別    名 MCLN1_HUMAN ; Mcoln 1 ; Mcoln1 ; MG 2 ; MG-2 ; MG2 ; ML 4 ; ML4 ; MLIV ; MST080 ; MSTP080 ; Mucolipidin ; Mucolipin-1 ; Mucolipin1 ; TRP ML1 ; TRPML1.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  免疫學  信號轉導  跨膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Pig, Cow, Rabbit, Sheep, Monkey, Cat, )
產(chǎn)品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 65kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human mucolipin 1
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a memberof the transient receptor potential (TRP) cation channel gene family. The transmembrane protein localizes to intracellular vesicular membranes including lysosomes, and functions in the late endocytic pathway and in the regulation of lysosomal exocytosis. The channel is permeable to Ca(2+), Fe(2+), Na(+), K(+), and H(+), and is modulated by changes in Ca(2+) concentration. Mutations in this gene result in mucolipidosis type IV. [provided by RefSeq, Oct 2009]

Function:
Cation channel probably playing a role in the endocytic pathway and in the control of membrane trafficking of proteins and lipids. Could play a major role in Ca(2+) transport regulating lysosomal exocytosis.

Subcellular Location:
Cell membrane. Late endosome membrane. Lysosome membrane.Entrez Gene: 57192 Human Entrez Gene: 94178 Mouse Entrez Gene: 288371 Rat Omim: 605248 Human SwissProt: Q9GZU1 Human SwissProt: Q99J21 Mouse Unigene: 567548 Human Unigene: 631858 Human Unigene: 8356 Mouse

Tissue Specificity:
Widely expressed in adult and fetal tissues.

DISEASE:
Defects in MCOLN1 are the cause of mucolipidosis type IV (MLIV) [MIM:252650]; also known as sialolipidosis. MLIV is an autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus. Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients. Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years. All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels. MLIV may be due to a defect in sorting and/or transport along the late endocytic pathway. MLIV is found at relatively high frequency among Ashkenazi Jews.

Similarity:
Belongs to the transient receptor (TC 1.A.4) family. Polycystin subfamily. MCOLN1 sub-subfamily.

Database links:

Entrez Gene: 57192 Human

Entrez Gene: 94178 Mouse

Entrez Gene: 288371 Rat

Omim: 605248 Human

SwissProt: Q9GZU1 Human

SwissProt: Q99J21 Mouse

Unigene: 567548 Human

Unigene: 631858 Human

Unigene: 8356 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.a6308.cn 北京博奧森生物技術有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
久久久SS麻豆欧美国产日韩 | 亚洲日韩中文字幕A∨ | 怡红院日本一道日本久久 | 屁屁国产第1页草草影院 | 奇米第四狠狠777高清秒播 | 高清一级毛片一本到免费观看 | 无码人妻免费—区二区三 | 亚洲精品白浆高清久久久久久 | 久久久精品国产亚洲成人满18免费网站 | 欧美一级特黄AAAAAAAA片在线看 | 成人国产欧美大片一区 | 五月丁香啪啪激情综合5109 | 99久久精品免费看国产一区二区三区 | 久久国产劲爆∧v内射 | 一级毛片免费播放 | 亚洲日韩在线男人视频网站 | 中文字幕人妻偷人伦在线视频 | 久久精品中文字幕第一页国产精品 | 国产又粗又猛又爽的视频国产 | 1级a的观看视频 | 国产精品久久国产三级国电话系列 | 日本有码在线中文字幕 | 亚洲精品国产A久久久久久 91手机在线视频观看 | 亚洲精品无码高潮喷水在 | 狠狠色噜噜狠狠狠777 | 久久中文骚妇内射 | 农村妇女牲交一级毛片 | 亚洲精品国产综合久久一线 | 永久黄网站色视频免费 | 欧美人与禽zoz0性伦交 | 中文字幕一区在线观看视频 | 在线无码一区二区三区不卡 | 又白又嫩毛又多15P 伦人伦 XXX国语对白 | 色欲TV国产亚洲AV麻豆 | 日本不卡高字幕在线2019 | 亚洲AV成人无码一二三在线观看 | 欧美最猛黑人xxxx黑人猛交 | 中文字幕+乱码+中文乱码www | 一本大道加勒比久久 | 业佘老头视频man4 | 亚洲精品无码av中文字幕网站 |