亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
高清欧美在线三级视频,韩国免费一级a一片在线播放
Rabbit Anti-mucolipin 3/BF350 Conjugated antibody (bs-18732R-BF350)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@bioss.com.cn
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-18732R-BF350
英文名稱 Rabbit Anti-mucolipin 3/BF350 Conjugated antibody
中文名稱 BF350標(biāo)記的粘脂蛋白3抗體
別    名 MCOLN 3 ; MCOLN3 ; FLJ11006 ; FLJ36629 ; MCLN3_HUMAN ; MCOLN 3 ; MCOLN3 ; MGC71509 ; Mucolipin-3 ; TRP ML3 ; TRPML3.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  神經(jīng)生物學(xué)  跨膜蛋白  細(xì)胞膜蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 64kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human mucolipin 3
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes one of members of the mucolipin cation channel proteins. Mutation studies of the highly similar protein in mice have shown that the protein is found in cochlea hair cells, and mutant mice show early-onset hearing loss and balance problems. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Nov 2011]

Function:
Cation channel probably playing a role in the endocytic pathway and in the control of membrane trafficking of proteins and lipids. Could play a major role in Ca2+ transport regulating lysosomal exocytosis.

Subunit:
Forms multimeric complexes. Interacts with PDCD6.

Subcellular Location:
Membrane.

Tissue Specificity:
Widely expressed in adult and fetal tissues.

DISEASE:
Mucolipidosis type IV (MLIV) [MIM:252650]: Autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus. Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients. Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years. All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels. MLIV may be due to a defect in sorting and/or transport along the late endocytic pathway. MLIV is found at relatively high frequency among Ashkenazi Jews.

Similarity:
Belongs to the transient receptor (TC 1.A.4) family.
Polycystin subfamily.
MCOLN1 sub-subfamily.

Database links:

Entrez Gene: 55283 Human

Omim: 607400 Human

SwissProt: Q5T4H5 Human

SwissProt: Q8TDD5 Human

Unigene: 535239 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.a6308.cn 北京博奧森生物技術(shù)有限公司
通過國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
美女脱18以下禁止看免费 | 国产又黄又爽胸又大免费视频 | 亚洲另类春色国产精品 | 国产99视频精品免视看7 | 女人扒开腿让男人狂桶30分钟 | 欧美高清视频www夜色资源网 | 91精品国产乱码久久无码 | 最近中文字幕国语免费高清6 | 文中字幕一区二区三区视频播放 | 色欲久久精品亚洲AV无码一区 | 天堂网在线最新版www | 97人视频国产在线观看 | 99精品一级欧美片免费播放 | h嗯啊巨肉寝室男男bl | 国产黄色网站在线观看 | 成人国产欧美大片一区 | 999国内精品永久免费观看 | 成人国产欧美大片一区 | 日本午夜精品一区二区三区电影 | 新普新京亚洲欧美日韩国产 | 欧美日韩中文字幕群交视频在线观看 | 国产成人剧情AV麻豆映画 | 偷拍殴美一区二区三区 | 免费观看国产网址你懂的 | 向日葵视频APP秋葵榴莲网站 | 精品国产乱码久久久久久呢 | 久久精品九九亚洲精品 | 久久精品国产亚洲AV影院 | 国产成人精选视频在线观看不卡 | √天堂资源地址在线官网 | 国内大量揄拍人妻在线视频 | 人善交video欧美 | 日韩欧美高清黄大片色成人精品香蕉在线看 | 久久久高清免费视频 | 国产偷窥盗摄一区二区 | 欧美精品在线一区二区三区 | 国产欧美日韩综合一区在线播放 | 99久久国产综合精品麻豆导演 | 毛片女人十八以上观看 | 99热成人精品国产免男男 | 日本爽爽爽爽爽爽在线观看免 |